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Anti-DPM3 Antibody

品牌：Antibodies

货号：

规格：100µg

货期：

应用：

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Anti-DPM3 Antibody

商品详情参考文献相关资料

Overview

Name:	Anti-DPM3 Antibody See all DPM3 primary antibodies
Description:	Goat polyclonal antibody to DPM3.
Applications:	ELISA, WB
Reactivity:	Human
Immunogen:	Synthetic peptide corresponding to Human DPM3 (internal region).
Sequence:	HDCEDAARELQSQ
Host:	Goat
Clonality:	Polyclonal
Isotype:	IgG
Conjugate:	Unconjugated
Purification:	Purified from goat serum by ammonium sulphate precipitation followed by antigen affinity chromatography using the immunizing peptide.
Concentration:	100 µg at 0.5 mg/ml.
Product Form:	Liquid
Formulation:	Supplied in Tris Buffered Saline, pH 7.30, with 0.02% Sodium Azide and 0.5% BSA.
Storage:	Shipped at 4°C. Upon delivery aliquot and store at -20°C. Avoid freeze / thaw cycles.

Target

Function:	Stabilizer subunit of the dolichol-phosphate mannose (DPM) synthase complex; tethers catalytic subunit DPM1 to the ER.
Involvement in Disease:	Congenital disorder of glycosylation 1O: A form of congenital disorder of glycosylation, a multisystem disorder caused by a defect in glycoprotein biosesynthesis and characterized by under-glycosylated serum glycoproteins. Congenital disorders of glycosylation result in a wide variety of clinical features, such as defects in the nervous system development, psychomotor retardation, dysmorphic features, hypotonia, coagulation disorders, and immunodeficiency. The broad spectrum of features reflects the critical role of N-glycoproteins during embryonic development, differentiation, and maintenance of cell functions. CDG1O patients have increased serum creatine kinase, dystrophic changes on muscle biopsy, and reduced O-mannosylation of alpha-dystroglycan.
Sequence Similarities:	Belongs to the DPM3 family.
Cellular locations:	Endoplasmic reticulum membrane.
Database Links:	Entrez Gene: 54344 Human Omim: 605951 Human SwissProt: Q9P2X0 Human Unigene: 110477 Human
Synonyms:	CDG1O Antibody Dolichol Phosphate Mannose Synthase subunit 3 Antibody Dolichol phosphate mannosyltransferase subunit 3 Antibody Dolichyl Phosphate beta D Mannosyltransferase subunit 3 Antibody Dolichyl phosphate mannosyltransferase polypeptide 3 Antibody DPM synthase complex subunit 3 Antibody DPM3 Antibody Mannose P Dolichol Synthase subunit 3 Antibody MPD synthase subunit 3 Antibody Prostin 1 Antibody
Information:	Target information shown above is from the UniProt Consortium.